Inherited epidermolysis bullosa: clinical and therapeutic aspects

Anais Brasileiros de Dermatologia

Vanessa Lys Simas Yamakawa Boeira¹  Erica Sales Souza¹  Bruno De Oliveira Rocha¹  Pedro Dantas Oliveira¹  Maria De Fátima Santos Paim De Oliveira¹  Vitória Regina Pedreira De Almeida Rêgo¹  Ivonise Follador¹ 

关键词: Epidermolysis bullosa;    Epidermolysis bullosa dystrophica;    Epidermolysis bullosa;    junctional;    Epidermolysis bullosa simplex;    Epidermólise bolhosa;    Epidermólise bolhosa distrófica;    Epidermólise bolhosa juncional;    Epidermólise bolhosa simples;   

DOI  :  10.1590/S0365-05962013000200001

来源: SciELO

【 摘 要 】

Inherited epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders that present with skin and, in some cases, mucosal fragility, predisposing patients to the development of blisters and/or erosions after minimal trauma or friction. Children with a recurrent history of these kinds of lesions or neonates that present them in the absence of another reasonable explanation should be investigated. Diagnosis must be based on clinical and histopathological findings. To date, management of inherited EB basically consists in avoiding traumas that trigger lesions, as well as preventing infection and facilitating healing of the wounds with the systematic use of bandages.

【 授权许可】

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