Pattern of inner retinal layers involvement in pigmented paravenous retinochoroidal atrophy as determined by SD-OCT: case report

Arquivos Brasileiros de Oftalmologia

Daniela Laura Melo Junqueira¹  Flavio Siqueira Santos Lopes¹  Luís Gustavo Biteli¹  Tiago Santos Prata¹ 

[1] ,Hospital Medicina dos OlhosSão Paulo SP ,Brazil

关键词: Atrophy;    Retinal ganglion cells;    Choroid;    Retina;    Retinal nerve fiber layer;    Tomography;    optical coherence;    Visual field;    Case report;    Atrofia;    Células ganglionares da retina;    Coroide;    Retina;    Camada de fibras nervosas da retina;    Tomografia de coerência óptica;    Campo visual;    Relato de caso;   

DOI  :  10.1590/S0004-27492013000600014

来源: SciELO

【 摘 要 】

Pigmented paravenous retinochoroidal atrophy is an ocular disease characterized by outer retina and choroidal atrophy often with overlying intraretinal bone spicule pigment deposition along the retinal veins. As a rare condition, there is scant information in the literature regarding the pattern of inner retinal layers involvement. We present a case of a 41-year-old white man initially referred for a glaucoma evaluation. Fundoscopy revealed patches of retinochoroidal atrophy and light pigmentation extending from the optic nerve head along the inferior-temporal retinal veins in both eyes. Using different spectral-domain optical coherence tomography (SD-OCT) protocols we identified a significant thinning of the inner retinal layers along the inferior-temporal veins, but with a lucid interval surrounding the optic nerve head. Standard automated perimetry revealed a superior absolute arcuate scotoma sparing the central fixation (good structure-functional correlation). This pattern of inner retinal layers involvement was not previously described. We believe SD-OCT added significantly to the anatomical description of this case. Physicians should consider these new anatomical findings and correlate them with functional status while assessing these patients.

【 授权许可】

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