A rare presentation of multiple sclerosis: Schilder's disease

Radiology Case Reports

Hajar Khattab, MD¹  Youssef Sakhy, MD²  Reda Taoussi, MD³  Omar Amriss, MD³  Hasna Belgadir, MD³  Nadia Moussali, MD³  Naima EL Benna, MD³  Aïcha Merzem, MD³ 

[1] Corresponding author.;Department of neurology, Ibn Rochd University Hospital, Casablanca, Morocco;Imaging Department, Ibn Rochd University Hospital, 1 quartier des hôpitaux, Casablanca, Morocco;

关键词: Schilder's disease;    Multiple sclerosis;    MRI;    Demyelinating;   

DOI  :  

来源: DOAJ

【 摘 要 】

Schilder's disease is a rare form of multiple sclerosis. It concerns mostly teenagers and young adults. The Clinical signs and symptoms might be atypical for early multiple sclerosis which often mimics intracranial neoplasm or abscess. Their coursemay be either progressive or relapsing and remitting, with a high sensitivity to steroids. The knowledge of this rare form ofmultiple sclerosis may help radiologists in assessing a precise diagnosis. We report the case of a young 22-year-old patientadmitted to the emergency room with an array of headache, vomiting and frontal syndrome. Magnetic resonance imaging shows2 bilateral demyelinating frontal areas. The patient was put under corticosteroids bolus with discreet improvement in her clinicalcondition. After 6 months of follow-up, we did not notice any real clinical improvement. Although Schilder's disease isconsidered to be a variant of Multiple Sclerosis, its clinical and imaging features behaves more like a demyelinating conditionwith its monophasic course with, however, serious clinical consequences if the treatment is delayed.

【 授权许可】

Unknown