Pulmonary Fibrosis in Children

Journal of Clinical Medicine

卷:8

Spyros Papiris¹  Effrosyne Manali¹  Pierre-Louis Léger²  Aurore Coulomb l’Hermine³  Nadia Nathan⁴  Laura Berdah⁴  Céline Delestrain⁴  Guillaume Thouvenin⁴  Annick Clement⁴  Hubert Ducou le Pointe⁵  Chiara Sileo⁵ 

[1] 2nd Pulmonary Medicine Department, General University Hospital “Attikon”, Medical School, National and Kapodistrian University of Athens, 12462 Athens, Greece;

[2] Intensive Care Unit, Armand Trousseau Hospital, AP-HP, 75012 Paris, France;

[3] Pathology Department, Armand Trousseau Hospital, AP-HP, 75012 Paris, France;

[4] Pediatric Pulmonology Department, Reference Center for Rare Lung Diseases (RespiRare), Armand Trousseau Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), 75012 Paris, France;

[5] Pediatric Radiology Department, Armand Trousseau Hospital, AP-HP, 75012 Paris, France;

关键词: pulmonary fibrosis;    interstitial lung disease;    children;    usual interstitial pneumonia;    nonspecific interstitial pneumonia;   

DOI  :  10.3390/jcm8091312

来源: DOAJ

【 摘 要 】

Pulmonary fibrosis (PF) is a very rare condition in children, which may be observed in specific forms of interstitial lung disease. None of the clinical, radiological, or histological descriptions used for PF diagnosis in adult patients, especially in situations of idiopathic PF, can apply to pediatric situations. This observation supports the view that PF expression may differ with age and, most likely, may cover distinct entities. The present review aims at summarizing the current understanding of PF pathophysiology in children and identifying suitable diagnostic criteria.

【 授权许可】

Unknown