期刊论文详细信息
Anais Brasileiros de Dermatologia
Primary systemic amyloidosis, acquired cutis laxa and cutaneous mucinosis in a patient with multiple myeloma
Fernanda Guedes Lavorato1  Maria De Fátima Guimarães Scotelaro Alves1  Juan Manuel Piñeiro Maceira1  Natasha Unterstell1  Laura Araújo Serpa1  Luna Azulay-abulafia1 
关键词: Amyloidosis;    Cutis laxa;    Mucinoses;    Multiple myeloma;    Amiloidose;    Cútis laxa;    Mieloma múltiplo;    Mucinoses;   
DOI  :  10.1590/abd1806-4841.20132531
来源: SciELO
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【 摘 要 】

A 57-year-old woman presented with periorbital ecchymoses, laxity in skin folds, polyneuropathy and bilateral carpal tunnel syndrome. A skin biopsy of the axillary lesion demonstrated fragmentation of elastic fibers, but with a negative von Kossa stain, consistent with cutis laxa. The diagnosis of primary systemic amyloidosis was made by the presence of amyloid material in the eyelid using histopathological techniques, besides this, the patient was also diagnosed with purpura, polyneuropathy, bilateral carpal tunnel syndrome and monoclonal gammopathy. She was diagnosed as suffering from multiple myeloma based on the finding of 40% plasma cells in the bone marrow, component M in the urine and anemia. The patient developed blisters with a clear content, confirmed as mucinosis by the histopathological exam. The final diagnoses were: primary systemic amyloidosis, acquired cutis laxa and mucinosis, all related to multiple myeloma.

【 授权许可】

CC BY-NC   
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