Cutaneous neonatal lupus with cutis marmoratatelangiectatica congenita-like lesions

Anais Brasileiros de Dermatologia

Flavia Trevisan¹  Paulo Rowilson Cunha¹  Clovis Antonio Lopes Pinto¹  Fernanda Gomes Cattete¹ 

关键词: Antibodies;    Autoantibodies;    Clinical diagnosis;    Congenital;    hereditary;    and neonatal diseases and abnormalities;    Diagnosis;    differential;    Lupus erythematosus;    systemic;    Anticorpos;    Auto-anticorpos;    Diagnostico clinico;    Diagnostico diferencial;    Doencas congenitas;    hereditarias e neonatais e anormalidades;    Lupus eritematoso sistemico;   

DOI  :  10.1590/abd1806-4841.20131832

来源: SciELO

【 摘 要 】

Neonatal lupus is a rare disease caused by the transplacental transfer of maternalautoantibodies to the foetus, characterized by transient clinical manifestations suchas cutaneous, haematological, and hepatobiliary events or permanent such ascongenital heart block. The typical cutaneous manifestations include erythematous,scaly, annular or arched lesions on the face, with slight central atrophy andphotosensitivy, clinically and histologically similar to subacute cutaneous lupus.However, in some cases, the lesions may resemble those in cutis marmoratatelangiectatica congenita, although this phenomenon is rare and only eight such caseshave been reported to date. We report a case of cutaneous neonatal lupus withatypical lesions on the limbs, which had a reddish-purple marbled appearance,resembling the lesions in cutis marmorata telangiectatica congenita.

【 授权许可】

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