Myocardial fibrosis in desmin-related hypertrophic cardiomyopathy

Journal of Cardiovascular Magnetic Resonance

Case Report

Tengyong Jiang¹  Daojun Hong²  Zhaoqi Zhang³  Qinyi Dai³  Yi He³ 

[1] Department of Cadiology, Beijing Anzhen Hospital, Capital Medical University, No. 2, Anzhen road, Chaoyang district, Beijing, China;Department of Neurology, Peking University First Hospital, Xishiku St 8#, 100034, Xicheng District, Beijing, China;Department of Radiology, Beijing Anzhen Hospital, Capital Medical University, No. 2, Anzhen road, Chaoyang district, Beijing, China;

关键词: Cardiomyopathy;    Cardiovascular Magnetic Resonance;    Late Gadolinium Enhancement;    Brain Natriuretic Peptide;    Myocardial Fibrosis;   

DOI  :  10.1186/1532-429X-12-68

 received in 2010-09-20, accepted in 2010-11-18,  发布年份 2010

来源: Springer

【 摘 要 】

Desmin-related myopathy (DRM) is known to cause different types of cardiomyopathy. Late gadolinium enhancement cardiovascular magnetic resonance (CMR) has been shown to identify fibrosis in ischemic and non-ischemic cardiomyopathies. We present a rare case of desmin-related hypertrophic cardiomyopathy, CMR revealed fibrosis in the lateral wall of the left ventricle. CMR is superior to conventional echocardiography for the detection of myocardial fibrosis in desmin-related cardiomyopathy, which may be useful to detect early cardiac involvement and predict the patient prognosis.

【 授权许可】

Unknown   
© He et al; licensee BioMed Central Ltd. 2010. This article is published under license to BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.