Perivascular epithelioid cell tumor of the rectum: report of a case and review of the literature

World Journal of Surgical Oncology

Case Report

Akinori Nozawa¹  Junko Ito¹  Norio Yukawa²  Munetaka Masuda²  Toshio Imada²  Yasushi Rino²  Mitsuyoshi Ota³  Amane Kanazawa³  Tadao Fukushima³  Shoichi Fujii³  Chikara Kunisaki³  Takashi Oshima³  Atsushi Ishibe³  Ten-i Godai³ 

[1] Department of Pathology, Yokohama City University Medical Center, 4-57 Urafune-cho Minami-ku, 232-0024, Yokohama-shi, Kanagawa-ken, Japan;Department of Surgery, Yokohama City University, 3-9 Fukuura, Kanazawa-ku, 236-0004, Yokohama-shi, Kanagawa-ken, Japan;Gastroenterological Center, Yokohama City University Medical Center, 4-57 Urafune-cho Minami-ku, 232-0024, Yokohama-shi, Kanagawa-ken, Japan;

关键词: Perivascular epithelioid cell tumor;    PEComa;    Transanal endoscopic microsurgery;   

DOI  :  10.1186/1477-7819-12-12

 received in 2013-06-14, accepted in 2013-12-25,  发布年份 2014

来源: Springer

【 摘 要 】

We report a case of perivascular epithelioid cell tumor arising in the rectum of a 55-year-old woman. The tumor was treated by transanal endoscopic microsurgery. After 1 year follow-up, the patient is alive with no radiologic or endoscopic evidence of recurrence. Perivascular epithelioid cell tumor is a rare mesenchymal tumor characterized by co-expression of melanocytic and smooth muscle markers. This rare tumor can arise in various organs, including the falciform ligament, uterus, uterine cervix, liver, kidney, lung, breast, cardiac septum, pancreas, prostate, thigh, and gastrointestinal tract. Perivascular epithelioid cell tumor of the gastrointestinal tract is very rare, with only 23 previously reported cases. We review the literature on perivascular epithelioid cell tumors arising in the gastrointestinal tract.

【 授权许可】

CC BY   
© Kanazawa et al.; licensee BioMed Central Ltd. 2014