Perivascular epithelioid cell tumor of the rectum: report of a case and review of the literature

World Journal of Surgical Oncology

Chikara Kunisaki³  Munetaka Masuda¹  Akinori Nozawa²  Junko Ito²  Toshio Imada¹  Yasushi Rino¹  Norio Yukawa¹  Mitsuyoshi Ota³  Tadao Fukushima³  Takashi Oshima³  Atsushi Ishibe³  Ten-i Godai³  Shoichi Fujii³  Amane Kanazawa³ 

[1] Department of Surgery, Yokohama City University, 3-9 Fukuura, Kanazawa-ku, Yokohama-shi, Kanagawa-ken 236-0004, Japan;Department of Pathology, Yokohama City University Medical Center, 4-57 Urafune-cho Minami-ku, Yokohama-shi, Kanagawa-ken 232-0024, Japan;Gastroenterological Center, Yokohama City University Medical Center, 4-57 Urafune-cho Minami-ku, Yokohama-shi, Kanagawa-ken 232-0024, Japan

关键词: Transanal endoscopic microsurgery;    PEComa;    Perivascular epithelioid cell tumor;   

Others  :  820558
DOI  :  10.1186/1477-7819-12-12

 received in 2013-06-14, accepted in 2013-12-25,  发布年份 2014

【 摘 要 】

We report a case of perivascular epithelioid cell tumor arising in the rectum of a 55-year-old woman. The tumor was treated by transanal endoscopic microsurgery. After 1 year follow-up, the patient is alive with no radiologic or endoscopic evidence of recurrence. Perivascular epithelioid cell tumor is a rare mesenchymal tumor characterized by co-expression of melanocytic and smooth muscle markers. This rare tumor can arise in various organs, including the falciform ligament, uterus, uterine cervix, liver, kidney, lung, breast, cardiac septum, pancreas, prostate, thigh, and gastrointestinal tract. Perivascular epithelioid cell tumor of the gastrointestinal tract is very rare, with only 23 previously reported cases. We review the literature on perivascular epithelioid cell tumors arising in the gastrointestinal tract.

【 授权许可】

   
2014 Kanazawa et al.; licensee BioMed Central Ltd.

【 图 表 】

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