Successful palliative resection of giant epimyocardial lymphatic malformation with 14 years of follow-up: a case report

BMC Cardiovascular Disorders

Case Report

Jouko Lohi¹  Sari Kivistö²  Sini Weckström³  Krista Heliö³  Tiina Heliö³ 

[1] Department of Pathology, HUSLAB, University of Helsinki and Helsinki University Hospital, Helsinki, Finland;Department of Radiology, University of Helsinki and Helsinki University Hospital, Helsinki, Finland;Heart and Lung Center, Helsinki University Hospital and University of Helsinki, Helsinki, Finland;

关键词: Benign heart tumors;    Lymphatic malformation;    Lymphangioma;    Cardiac surgery;    Case report;   

DOI  :  10.1186/s12872-023-03449-8

 received in 2023-07-05, accepted in 2023-08-14,  发布年份 2023

来源: Springer

【 摘 要 】

BackgroundPrimary tumors of the heart are a rare phenomenon. Lymphatic malformations are congenital anomalies of the lymphatic system that tend to grow progressively. Lymphatic malformations are typically found in the cervical and axillary regions and found on pediatric patients. We report a 40-year-old woman with giant epimyocardial lymphatic malformation.Case presentationA 40-year-old woman was assessed due to suspected traumatic cardiac tamponade. Computed tomography of the heart and cardiac magnetic resonance imaging were compatible with either a large pericardial hemangioma or angiosarcoma. The tumor infiltrated deeply into the myocardium and could only be partially resected. Histopathological diagnosis was a cardiac lymphatic malformation with micro- and macrocystic components. The patient has remained asymptomatic for fourteen years after the surgery. In the latest follow-up, her left ventricular function had remained normal and the maximum thickness of the residual tumor had regressed.ConclusionsEven when a complete removal of a cardiac lymphatic malformation is not possible, a debulking procedure can yield a good long-term result.

【 授权许可】

CC BY   
© BioMed Central Ltd., part of Springer Nature 2023

【 图 表 】

Fig. 11