Primary renal leiomyosarcoma with a tumor thrombus in the inferior vena cava

IJU Case Reports

article

Mikio Konno¹  Takahiro Osawa¹  Kiyohiko Hotta¹  Ai Shimizu²  Takashige Abe¹  Ryuji Matsumoto¹  Hiroshi Kikuchi¹  Nobuo Shinohara¹ 

[1] Department of Urology, Hokkaido University Hospital;Department of Surgical Pathology, Hokkaido University Hospital

关键词: kidney;    leiomyosarcoma;    thrombus;    vena cava;   

DOI  :  10.1002/iju5.12396

学科分类：社会科学、人文和艺术（综合）

来源: Wiley

【 摘 要 】

Introduction We report a rare case of primary renal leiomyosarcoma with a tumor thrombus in the inferior vena cava. Case presentation A 54-year-old woman presented with right flank pain and abdominal distension. Physical examination findings were unremarkable. Abdominal computed tomography revealed a heterogeneously enhancing right solid renal mass with a thrombus in the renal vein extending into the inferior vena cava. Magnetic resonance imaging demonstrated a renal tumor with a thrombus about 4 cm below the hepatic vein. Chest computed tomography and bone scintigraphy were negative. The patient underwent right radical nephrectomy and vena cava thrombectomy. Histophathologic evaluation of the resected tumor confirmed the diagnosis of leiomyosarcoma. She underwent no adjuvant therapy. Seven months after surgery, the patient died following a 2-month history of multiple pulmonary and hepatic metastases. Conclusion This report highlights the importance of considering the possibility of renal leiomyosarcoma invasion to the inferior vena cava, similar to renal cell carcinoma.

【 授权许可】

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