A rare case of leiomyosarcoma of the inferior vena cava in a 32-year-old patient

Precision Radiation Oncology

article

Paulo César Rosenbaum¹  Aroldo Henrique da Silva Boigues¹  Fernando Zambelli Tassone¹  Isabela Martinhão¹  João Italo Fortaleza de Melo¹  Raphael Oliveira Ramos Franco Netto²  Victor Augusto Ramos Fernandes²  Messias Villa Mendonça¹  Lindyane de Souza Freitas Melo¹  Cindy Liberato Rocha Castilhos¹  Leonardo Gattass Ferreira¹  Luiz Dias Dutra¹ 

[1] Radiology and Diagnostic Imaging Center-CERDIL;Laboratory of Tissue Morphology, Faculty of Medicine of Jundiaí-FMJ

关键词: abdominal neoplasm;    abdominal pain;    diagnostic imaging;    leiomyosarcoma;    radiology;    vena cava;   

DOI  :  10.1002/pro6.1118

学科分类：社会科学、人文和艺术（综合）

来源: Wiley

【 摘 要 】

Leiomyosarcoma is a malignant tumor that develops from the smooth muscle constituents of the middle layer in veins, usually affecting the inferior vena cava (IVC); however, this disease is observed in older patients. In this report, we describe a rare case of a 32-year-old female patient who presented with leiomyosarcoma. Initially, the patient complained of moderate-intensity pain in the abdominal region of the right hypochondrium and nausea, worsening postprandial starting 6 days earlier. Abdominal ultrasonography showed a heterogeneous hypoechoic expansive formation, with lobulated contours and ill-defined limits in the projection of the IVC. Inferior vena cavography, showed obliteration of the vessel in almost all of its extensions. Magnetic resonance examination showed a large expansive lesion occupying the IVC. The lesion was resected, and the specimen was sent for anatomopathological analysis, which showed a leiomyosarcoma of the IVC. Patients with leiomyosarcoma have a poor prognosis, and early diagnosis and complete resection with free surgical margins are the only chance of long-term survival. The report stands out due to the appearance of this condition in a young patient with no family history of this disease or other predisposing carcinogenic pathologies.

【 授权许可】

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