Development of lymphangioleiomyomatosis in a female patient with Sjö gren's disease: a review of literature and a case report

Современная ревматология

V. I. Vasiliev¹  Yu. I. Khvan²  S. G. Palshina² 

[1] MEDSI Clinic;V.A. Nasonova Research Institute of Rheumatology;

关键词: sjögren's disease;    sjögren's syndrome;    lymphangioleiomyomatosis;    cystic lung diseases;    clinical case;   

DOI  :  10.14412/1996-7012-2019-2-119-123

来源: DOAJ

【 摘 要 】

Cystic and bullous lung transformation occurs in diseases of various origins: neoplastic, genetically determined, rheumatic, lymphoproliferative, and infectious diseases. The paper presents a review of the literature and a clinical case of a young female patient with a long history of Sjögren's disease. Fifteen years after the onset of the disease, the patient developed cystic and bullous lung transformation and renal angiomyolipoma, which are regarded as a manifestation of probable lymphangioleiomyomatosis.

【 授权许可】

Unknown