Cystoid macular edema in a patient with Danon disease

Indian Journal of Ophthalmology

关键词: Malignant glaucoma;    pseudophakic;    surgical management;    zonulo-hyaloido-vitrectomy;    Automated retinal imaging;    diabetic retinopathy;    screening;    Low vision;    low vision aids;    quality of life;    Children;    congenital cataract;    hydrophobic acrylic intraocular lens;    intraocular lens implantation;    myopic shift;    polymethyl methacrylate;    Cost-effectiveness;    glaucoma;    pharmacoeconomics;    External limiting membrane;    macular hole;    predictors;    Optic nerve head drusen;    optical coherence tomography;    papilledema;    pseudopapilloedema;    Crowding;    logMAR chart;    refractive error;    screening;    visual acuity;    Acute retinal pigment epithelitis;    multifocal electroretinogram;    optical coherence tomography;    Anterior chamber;    intraocular parasite;    Linguatula serrata (tongue worm);    subluxated lens;    vitrectomy;    Carbonic anhydrase inhibitor;    Danon disease;    ERG;    retinal disease;    SD-OCT;   

DOI  :  10.4103/0301-4738.109524

来源: DOAJ

【 摘 要 】

To report a patient with Danon retinopathy with cystoid macular edema treated with topical dorzolamide 2% eye drops and oral acetazolamide. A 37-year-old Caucasian man with Danon disease treated with topical and oral carbonic anhydrase inhibitors participated in the study. Examinations performed before and during treatment included visual acuity (VA), spectral-domain optical coherence tomography, and electroretinography. Following total 48 weeks of treatment, VA decreased from 20/30 OD, 20/200 OS, to 20/40 OD, CF OS. The mean central retinal thickness was unchanged from baseline 263 μm OD , 226 μm OS, after treatment 283 μm OD and 202 μm OS. In our case, carbonic anydrase inhibitors were not effective. However, a general recommendation cannot be given based on a single case.

【 授权许可】

Unknown