Transarterial coil embolization of an aortic root pseudoaneurym in a patient with Loeys-Dietz syndrome: a case report

CVIR Endovascular

Jacqueline Saw¹  Manraj Heran²  Robert D’Ortenzio³  Ravjot Dhatt³  Leandro Cardarelli-Leite⁴ 

[1] Department of Cardiology, University of British Columbia;Department of Radiology, BC Children’s Hospital;Department of Radiology, University of British Columbia;Department of Radiology, Western University;

关键词: Aortic aneurysm;    Aortic pseudoaneurysm;    Bentall;    Interventional procedures;    Loeys-Dietz;    Connective tissue disease;   

DOI  :  10.1186/s42155-020-00184-5

来源: DOAJ

【 摘 要 】

Abstract Background Loeys-Dietz syndrome (LDS) is a rare autosomal-dominant connective tissue disorder characterized by arterial aneurysms and vascular friability. Surgical intervention for LDS patients carries significant morbidity and mortality. Currently, the standard management of aortic root pseudoaneurysms is surgical intervention. Case presentation A 20 year old male with LDS presented with a progressively enlarging ascending aortic aneurysm. He underwent a Bentall-type aortic root replacement complicated by a 20 mm aortic root anastomotic pseudoaneurysm. Due to the patient’s high risk for repeat surgical intervention, he underwent successful transarterial coil embolization of his aortic root pseudoaneurysm without complication. Conclusions Coil embolization may provide an alternative treatment for patients presenting with aortic root pseudoaneurysm who are high risk for traditional surgical treatment, such as those with connective tissue disease.

【 授权许可】

Unknown