Idiopathic pleuroparenchymal fibroelastosis: The first case to be managed with a successful lung transplant at King Faisal Specialist Hospital and Research Center, Riyadh

Annals of Thoracic Medicine

关键词: Interstitial lung disease;    lung transplant;    pleuroparenchymal fibroelastosis;   

DOI  :  10.4103/atm.ATM_106_18

来源: DOAJ

【 摘 要 】

Idiopathic Pleuro-Parenchymal Fibroelsatosis (PPFE) is a rare, progressive and recently recognized subtype of idiopathic interstitial lung disease with no recorded successful treatment other than lung transplant. We report a case of idiopathic pleuroparenchymal fibroelastosis from the Middle East, managed successfully by bilateral lung transplant performed on a 26 year old Saudi male.

【 授权许可】

Unknown