The case of idiopathic pleuroparenchymal fibroelastosis diagnosed by transbronchial biopsy

Eurasian Journal of Pulmonology

关键词: Idiopathic;    pleuroparenchymal fibroelastosis;    transbronchial biopsy;   

DOI  :  10.4103/ejop.ejop_12_18

来源: DOAJ

【 摘 要 】

Pleuroparenchymal fibroelastosis (PPFE) is claasified in idiopathic interstitial pneumonitis group is rarely seen. Etiology and pathophysiology of this entity are not completely understood. The prognosis is poor, and there is no effective treatment except for lung transplantation. Here, we presented a case of PPFE diagnosed by transbronchial biopsy through fiberoptic bronchoscopy and its histopathological and clinicoradiological features.

【 授权许可】

Unknown