Ewing’s Sarcoma of the Cranial Vault Revealed by Macrocrania

Asian Journal of Oncology

卷:8

Fabrice Senghor¹  Momar Codé Ba²  Seydou Boubacar Badiane²  Mohameth Faye²  Abdoulaye Diop³  Lamine Thiam⁴ 

[1] Anatomical Pathology, Unit Peace Hospital of Ziguinchor, Ziguinchor, Senegal;

[2] Neurosurgery Department, Fann Teaching Hospital, Dakar, Senegal;

[3] Neurosurgery Unit, Ziguinchor Peace Hospital, Ziguinchor, Senegal;

[4] Pediatrics Department, Ziguinchor Peace Hospital, Ziguinchor, Senegal;

关键词: ewing’s sarcoma;    cranial vault;    macrocrania;   

DOI  :  10.1055/s-0040-1713318

来源: DOAJ

【 摘 要 】

Ewing’s sarcomas are a heterogeneous group of aggressive tumors affecting mostly children and young adults. They account for 10% of primary malignancies of the bones and 3% of all malignancies in children. They mainly affect the long bones, pelvis, and ribs. Cranial vault localization is extremely rare and indeed account for less than 1% of all localizations in the body. We are reporting the unusual case of a 3-year-old child who presented to our unit with a macrocrania which had been evolving for 2 months prior to his admission, associated with sporadic vomiting and a right frontal swelling that was gradually installed. The cerebral computed tomography scan showed a right frontoparietal lytic tissular process, heterogeneously enhanced after injection of contrast material; with dural invasion and intraparenchymal extension. The child was biopsied and the pathological examination concluded Ewing’s sarcoma. The evolution was fatal with the passing of the child 2 weeks after the biopsy.

【 授权许可】

Unknown