Moyamoya disease: report of three cases in Brazilian patients

Arquivos de Neuro-Psiquiatria

ClÉlia Maria Ribeiro Franco¹  Marcia Maiumi Fukujima²  Roberto De MagalhÃes Carneiro De Oliveira¹  Alberto Alain Gabbai² 

[1] ,Universidade Federal de São Paulo Escola Paulista de Medicina Department of Neurology and NeurosurgerySão Paulo,Brazil

关键词: moyamoya disease;    adult;    chronic occlusive cerebrovascular disorder;    stroke;    doença de moyamoya;    adulto;    doença cerebrovascular;    acidente vascular cerebral;   

DOI  :  10.1590/S0004-282X1999000300005

来源: SciELO

【 摘 要 】

Moyamoya disease (MMD) is a chronic occlusive cerebrovascular disease of unknown etiology reported mainly in the Japanese. Most cases occur in children. The disease is rare in non-Oriental adults manifesting itself mostly as intracerebral hemorrhages. We describe MMD in 2 non-Oriental young adults and one adolescent that developed cerebral infarctions. The adults were medicated with aspirin and no medication was given to the adolescent. All patients did not deteriorate in a follow-up period from 1 to 4 years. Although rare, MMD is an important cause of stroke in young individuals and may well be underreported: only 18 patients have been reported till 1997 in Brazil. Neurologists should include MMD in differential diagnosis of ischemic and hemorrhagic strokes in young adults.

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