Sickle cell retinopathy: diagnosis and treatment

Arquivos Brasileiros de Oftalmologia

Maria Teresa Brizzi Chizzotti Bonanomi¹  Marcelo Mendes Lavezzo¹ 

[1] ,Universidade de São Paulo School of Medicine São Paulo SP ,Brazil

关键词: Retinal diseases;    Retinal diseases;    Hemoglobin;    sickle;    Sickle cell trait;    Hemoglobin SC disease;    Vitreoretinal surgery;    Doenças retinianas;    Doenças retinianas;    Hemoglobina falciforme;    Traço falciforme;    Doença da hemoglobina SC;    Cirurgia vitreorretiniana;   

DOI  :  10.1590/S0004-27492013000500016

来源: SciELO

【 摘 要 】

Hemoglobinopathies are a group of inherited disorders characterized by quantitative or qualitative malformations of hemoglobin (Hb). Some of these diseases present vaso-occlusive phenomena that are responsible for high morbidity in clinical and/or ophthalmologic terms. Diagnosis of hemoglobinopathies is performed exclusively through hemoglobin electrophoresis. From the ophthalmologic perspective, the most important representative of this group of diseases is sickle cell retinopathy, which presents a wide spectrum of fundus manifestations and may even lead to irreversible vision loss if not properly diagnosed and treated. The aim of this review is to present the classification of sickle cell retinopathy and to describe current management and future perspectives for its treatment, taking into consideration the clinical management of these patients.

【 授权许可】

CC BY   
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