Proximal-type epithelioid sarcoma - Case report

Anais Brasileiros de Dermatologia

Luciana Mendes Dos Santos¹  Lisiane Nogueira¹  Christiane Yuri Matsuo¹  Carolina Talhari¹  Monica Santos¹ 

关键词: Diagnosis;    Diagnosis;    differential;    Sarcoma;    Therapeutics;    Diagnostico;    Diagnostico diferencial;    Sarcoma;    Terapeutica;   

DOI  :  10.1590/abd1806-4841.20131922

来源: SciELO

【 摘 要 】

Epithelioid sarcoma, first described by Enzinger in 1970, is a rare soft-tissue sarcoma typically presenting as a subcutaneous or deep dermal mass in distal portions of the extremities of adolescents and young adults. In 1997, Guillou et al. described a different type of epithelioid sarcoma, called proximal-type epithelioid sarcoma, which is found mostly in the pelvic and perineal regions and genital tracts of young to middle-aged adults. It is characterized by a proliferation of epithelioid-like cells with rhabdoid features and the absence of a granuloma-like pattern. In this paper we present a case of proximal-type epithelioid sarcoma with an aggressive clinical course, including distant metastasis and death nine months after diagnosis.

【 授权许可】

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