Herlyn-Werner-Wunderlich syndrome: a case report

Revista Brasileira de Ginecologia e Obstetrícia

Pedro Salomao Piccinini¹  John Doski¹ 

关键词: Müllerian ducts;    Vagina;    Uterus;    Kidney;    Ductos paramesonéfricos;    Vagina;    Útero;    Rim;   

DOI  :  10.1590/SO100-720320150005077

来源: SciELO

【 摘 要 】

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital disorder of the Müllerian ducts in which there is uterus didelphys, obstructed hemivagina and unilateral renal agenesis. The most common presentation is an abdominal mass secondary to hematocolpos, pain and dysmenorrhea. However, in some cases, such as the one we present here, menses are normal due to an obstructed hemivagina, and diagnosis can be delayed. We describe evaluation and surgical management of a 13-year-old girl with this condition who was diagnosed by computed tomography (CT) scan and confirmed by pelvic ultrasound and surgical exploration, as well as a review of the literature.

【 授权许可】

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