Thermostability of α‐mannosidase in plasma from cystic fibrosis patients and carriers

FEBS Letters

Jacobsen, Helle¹  Kohlschütter, Alfried¹ 

[1] Laboratory of Pediatric Clinical Neurochemistry, Universitätskinderklinik, Martinistr. 52, 2000 Hamburg, FRG

关键词: Human disease;    Cystic fibrosis;    Pathogenetic mechanism;    Lysosomal enzyme;    α-Mannosidase;    CF;    cystic fibrosis;   

DOI  :  10.1016/0014-5793(82)80607-8

学科分类：生物化学/生物物理

来源: John Wiley & Sons Ltd.

【 摘 要 】

We investigated the thermostability at 41 °C of human plasma α-mannosidase in two cystic fibrosis patients, one carrier, and two healthy adults. We could not confirm the reported differences between these groups of subjects.

【 授权许可】

Unknown