Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon’s technique

Radiation Oncology

Stéphane Supiot⁴  Marc-André Mahé¹  Nadège Corradini⁵  Christine Haie-Meder³  Sophie Dumoucel²  Charlotte Demoor-Goldschmidt¹ 

[1] Faculty of Medicine, University of Nantes, Nantes, France;Department of Pediatric Oncology, Institut Gustave Roussy, 39, rue Camille Desmoulins, Villejuif, 94805, France;Department of Brachytherapy, Institut Gustave Roussy, 39, rue Camille Desmoulins, Villejuif, 94805, France;Department of Radiotherapy, Institut de Cancérologie de l’Ouest- René Gauducheau, Bd J Monod, Nantes, 44800, St-Herblain, France;Department of Pediatric Oncology, Centre Hospitalier Universitaire, Place Ricordeau, Nantes, France

关键词: Sphincter preservation;    Anus;    External beam radiation therapy;    Brachytherapy;    Rhabdomyosarcoma;   

Others  :  1226194
DOI  :  10.1186/s13014-015-0413-9

 received in 2015-01-02, accepted in 2015-04-21,  发布年份 2015

【 摘 要 】

Rhabdomyosarcoma (RMS) is the most common sarcoma in paediatric patients. A perianal site is unusual and is associated with a low cure rate. The few cases of reported perianal RMS have been associated with sequelae. Here, we report the case of a 29-month-old male child who received sequential treatment by surgery, chemotherapy and radiotherapy inspired by Papillon’s irradiation of adult anal/low-rectum cancers (including external beam radiotherapy in the gynecological exam position followed by brachytherapy) and who remains in complete remission 49 months post treatment with no sphincter or other anorectal disorders.

【 授权许可】

   
2015 Demoor-Goldschmidt et al.; licensee BioMed Central.

【 图 表 】

Figure 1.

【 参考文献 】

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