Melanotic neuroectodermal tumor of infancy in an African-indigenous patient from the Amazon: a case report

Head & Face Medicine

Fabrício Mesquita Tuji¹  João de Jesus Viana Pinheiro⁴  Sérgio de Melo Alves³  José Thiers Carneiro²  Thiago Pastor da Silva Pinheiro¹ 

[1] Oral radiology department, Dentistry posgraduation program, Federal University of Pará, Belém, PA, Brazil;Ophyr Loyola Hospital, Belém, PA, Brazil;Dentistry posgraduation program, Federal University of Pará, Belém, PA, Brazil;Oral Pathology department, Dentistry posgraduation program, Federal University of Pará, Belém, PA, Brazil

关键词: Imaging features;    Progonoma;    Melanotic neuroectodermal tumor of infancy;    Infant;   

Others  :  813638
DOI  :  10.1186/1746-160X-9-35

 received in 2012-07-11, accepted in 2013-11-06,  发布年份 2013

【 摘 要 】

Melanotic neuroectodermal tumor of infancy (MNTI) is a rare condition that occurs normally in the anterior maxilla of infants aged <1 year. The use of clinical and imaging tools for MNTI is extremely important to prevent problems with function as well as the aesthetic features in a breastfeeding child. Brazil is a multiethnic country with a poor epidemiological policy and little data to track the incidence of certain diseases, including MNTI. It is important to study this pathology with ethnicity as a factor to improve the current epidemiological programs and establish better post-treatment management. This paper describes a case of a 2-month-old male of African-indigenous descent and Brazilian Amazon residency, who presented to our unit in 2009 with a history of an expanding mass involving the anterior maxilla. Clinical and computerized tomography scans were used to diagnose the mass as MNTI, which was removed by total excision. A biopsy later confirmed the MNTI diagnosis.

【 授权许可】

   
2013 Pinheiro et al.; licensee BioMed Central Ltd.

【 图 表 】

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