Left pulmonary artery banding to repair ipsilateral diffuse pulmonary arteriovenous fistula

Journal of Cardiothoracic Surgery

Hiraku Doi¹  Tadashi Ikeda²  Tomohiro Nakata²  Fumitoshi Tsurumi¹  Shiro Baba¹  Kentaro Akagi¹  Takuya Hirata¹ 

[1] Department of Pediatrics, Graduate School of Medicine, Kyoto University, 54 Kawahara-cho, Shogoin, Sakyo-ku, Kyoto City, Kyoto, 6068507, Japan;Department of Cardiovascular Surgery, Graduate School of Medicine, Kyoto University, Kyoto, Japan

关键词: Pulmonary artery banding;    Diffuse type;    Pulmonary arteriovenous fistula;   

Others  :  1152935
DOI  :  10.1186/1749-8090-7-77

 received in 2012-04-06, accepted in 2012-07-18,  发布年份 2012

【 摘 要 】

Congenital pulmonary arteriovenous fistula (PAVF) is a rare disease which causes hypoxemia by shunting deoxygenated blood from the pulmonary artery into pulmonary venous return. Lung transplantation is the most effective therapy to treat severe, diffuse PAVF. However, the availability of lungs for transplantation is limited in most parts in the world. For patients with diffuse PAVF affecting only one side of the lungs, ipsilateral pulmonary artery banding (PAB) is an effective treatment, but not yet standard of care. We report successful treatment of a patient with diffuse left-sided PAVF with PAB. We believe that PAB is an effective therapy for severe unilateral PAVF and may serve as a bridge to lung transplantation.

【 授权许可】

   
2012 Hirata et al.; licensee BioMed Central Ltd.

【 图 表 】

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