Burkitts’s lymphoma – an atypical presentation

BMC Pediatrics

Andreas Nydegger¹  Maja Beck-Popovic²  Nicolas von der Weid²  Farah Ziade¹ 

[1] Pediatric Gastroenterology Unit, Department of Pediatrics, University of Lausanne, Centre Hospitalier Universitaire Vaudois, Rue du Bugnon 46, CH-1011, Lausanne, Switzerland;Pediatric Hematology/Oncology Unit, Department of Pediatrics, University of Lausanne, Centre Hospitalier Universitaire Vaudois, Rue du Bugnon 46, CH-1011, Lausanne, Switzerland

关键词: Krukenberg tumor;    Epstein barr virus;    Adolescent;    Stomach;    Gastric;    Burkitt’s lymphoma;   

Others  :  1170714
DOI  :  10.1186/1471-2431-12-113

 received in 2012-05-01, accepted in 2012-07-30,  发布年份 2012

【 摘 要 】

Background

In female adolescents and young adults, malignancies of the genital tract are the most frequent type of cancer, closely followed by Hodgkin’s and non-Hodgkin’s lymphomas.

Case Presentation

We report an unusual case of sporadic Burkitt’s lymphoma (BL) presenting with massive bilateral ovarian infiltration, peritoneal carcinomatosis and diffuse nodular lesions of the stomach and the intestine mimicking Krukenberg tumor. Diagnostic biopsies were obtained by endoscopy of the upper gastrointestinal tract. With intensive chemotherapy, complete remission was rapidly achieved, without life-threatening tumor lysis syndrome.

Conclusion

Besides metastatic gastric adenocarcinoma, BL is an important differential diagnosis in adolescents presenting with Krukenberg tumor.

【 授权许可】

   
2012 Ziade et al.; licensee BioMed Central Ltd.

【 图 表 】

Figure 1.

Figure 2.

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