Polycystic liver disease with right pleural effusion

1st International Conference on Tropical Medicine and Infectious Diseases (ICTROMI) Faculty of Medicine Universitas Sumatera Utara

Anggreini, A.Y.^1 ; Dairi, L.B.^1

Division of Gastroenterohepatology, Department of Internal Medicine, Haji Adam Malik Hospital, Universitas Sumatera Utara, North Sumatera, Medan, Indonesia^1

关键词: Autosomal dominants;    Case reports;    Liver disease;    Pleural effusion;    Treatment conditions;   

Others  :  https://iopscience.iop.org/article/10.1088/1755-1315/125/1/012211/pdf
DOI  :  10.1088/1755-1315/125/1/012211

来源: IOP

【 摘 要 】

Polycystic liver disease (PCLD) is a condition in which multiple cysts form in the hepatic parenchyma. The polycystic liver disease is also an autosomal dominant disorder (ADPLD) caused by a mutation in a gene that encodes a protein hepatocystin. PCLD has a prevalence count of 1:200,000 people in the people of America. PCLD occurs ± 24% of patients in the third decade of age to 80% by the sixth decade. Women tend to get larger cysts and more and correlated with the number of pregnancies. The following case report of a woman, 51-years-old who was treated at Haji Adam Malik hospital Medan with a diagnosis of polycystic liver disease with right pleural effusion. Some literature has reported complications of the polycystic liver disease but rarely reported with pleural effusion presentation. The patient had already undergone a puncture of pleural fluid and after three weeks of treatment condition of the patient improved and permitted to be outgoing patient.