Anomalous Cord From the Raphe of a Congenitally Bicuspid Aortic Valve to the Aortic Wall Producing Either Acute or Chronic Aortic Regurgitation

JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY

卷:63

Article

Vowels, Travis J.¹  Gonzalez-Stawinski, Gonzalo V.²  Ko, Jong M.¹  Trachiotis, Gregory D.^3,4  Roberts, Brad J.¹  Roberts, Charles S.⁵  Roberts, William C.^1,6,7 

[1] Baylor Univ, Med Ctr Dallas, Baylor Heart & Vasc Inst, Dallas, TX 75246 USA

[2] Baylor Univ, Med Ctr, Dept Cardiothorac Surg, Dallas, TX 75246 USA

[3] George Washington Univ, Med Ctr, Div Cardiothorac Surg, Washington, DC 20037 USA

[4] Vet Affairs Med Ctr, Washington, DC 20422 USA

[5] Trident Med Ctr, Palmetto Cardiovasc & Thorac Associates, Charleston, SC USA

[6] Baylor Univ, Med Ctr, Dept Internal Med, Div Cardiol, Dallas, TX 75246 USA

[7] Baylor Univ, Med Ctr, Dept Pathol, Dallas, TX 75246 USA

关键词: aortic regurgitation;    bicuspid aortic valve;    congenital heart disease;   

DOI  :  10.1016/j.jacc.2013.09.030

来源: Elsevier

【 摘 要 】

Objectives This report calls attention to an unappreciated cause of both acute and chronic aortic regurgitation (AR). Background Although stenosis develops in most patients with a congenitally bicuspid aortic valve (BAV), in others with this anomaly, pure AR (no element of stenosis) develops, some in the absence of infection or other clear etiology. Methods We describe 5 men who underwent aortic valve replacement for pure AR associated with a BAV containing an anomalous cord attaching the raphe of the conjoined cusp near its free margin to the wall of the ascending aorta cephalad to the sinotubular junction. Results Three of these 5 patients had a history of progressive dyspnea, and the anomalous cord, which was intact at operation, appeared to cause chronic AR by preventing proper coaptation of the 2 aortic valve cusps. The other 2 patients heard a pop during physical exertion and immediately became dyspneic, and at operation, the anomalous cord was found to have ruptured. Prolapse of the conjoined aortic valve cusp toward the left ventricular cavity resulted in severe acute AR. Conclusions This variant of the purely regurgitant BAV may cause either chronic AR (when the anomalous cord does not rupture) or acute severe AR (when the cord ruptures). (C) 2014 by the American College of Cardiology Foundation

【 授权许可】

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