Desmoplastic small round cell tumor: a case report and review of the literature

World Journal of Surgical Oncology

Case Report

Jie Zhao¹  Xiaoming Xing¹  Jing Yu²  Shibao Fang²  Xiang Li² 

[1] Department of Pathology, Affiliated Hospital of Medical College Qingdao University, 16 Jiangsu Road, 266003, Qingdao, China;Department of Ultrasound, Affiliated Hospital of Medical College Qingdao University, 266003, Qingdao, China;

关键词: Desmoplastic small round cell tumor;    Imaging;    Pathology;   

DOI  :  10.1186/1477-7819-12-9

 received in 2013-09-12, accepted in 2013-12-27,  发布年份 2014

来源: Springer

【 摘 要 】

Desmoplastic small round cell tumor is a rare malignant tumor that has a poor prognosis. It affects predominantly young males. In the current report, a 14-year-old male patient was admitted to the hospital for evaluation of abdominal distension, and abdominal pain. Imaging examination revealed a high prevalence of multiple intraperitoneal and liver parenchymal cystic and solid tumors. After an explorative surgery, the pathological findings confirmed the presentation of desmoplastic small round cell tumor. Diagnosis of desmoplastic small round cell tumor could easily have been overlooked since there was no specific evidence for this condition available in the clinical and imaging examinations. In the present study, ultrasound examination detected solid cystic masses, which suggested the presence of necrosis and hemorrhage. Immunohistochemistry and cytogenetic studies confirmed the diagnosis of desmoplastic small round cell tumor in this patient.

【 授权许可】

Unknown   
© Li et al.; licensee BioMed Central Ltd. 2014. This article is published under license to BioMed Central Ltd. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.