Primary adrenal leiomyosarcoma with lymph node metastasis: a case report

World Journal of Surgical Oncology

Case

Noriyoshi Miura¹  Nozomu Tanji¹  Tomoya Onishi¹  Toshio Kakuda¹  Tadahiko Kikugawa¹  Terutaka Noda¹  Yutaka Yanagihara¹  Riko Kitazawa² 

[1] Department of Urology, Ehime University Graduate School of Medicine, 454 Shitsukawa, 791-0295, Toon, Ehime, Japan;Division of Diagnostic Pathology, Ehime University Graduate School of Medicine, 454 Shitsukawa, 791-0295, Toon, Ehime, Japan;

关键词: Primary adrenal leiomyosarcoma;    IVC reconstruction;    Adrenalectomy;   

DOI  :  10.1186/s12957-016-0936-z

 received in 2015-12-25, accepted in 2016-06-28,  发布年份 2016

来源: Springer

【 摘 要 】

BackgroundLeiomyosarcomas typically originate in smooth muscle cell. Leiomyosarcoma potentially arising from the adrenal gland is an extremely rare mesenchymal tumors associated with delayed diagnosis and poor prognosis.Case presentationA 34-year-old man visited our department complaining of right hypochondriac pain. Computed tomography demonstrated a solid mass measuring 5.2 cm in diameter above the right kidney, corresponding to the right adrenal gland, and a lymph node mass, which appeared to have invaded the IVC wall. Right adrenalectomy and lymphadenectomy were performed. A microscopic examination revealed primary adrenal leiomyosarcoma with lymph node metastasis. No adjuvant therapy was performed, and the patient remains recurrence-free at 10 months postoperatively.ConclusionsWe experienced a very rare case of primary adrenal leiomyosarcoma.Aggressive surgical resection including vascular reconstruction may be associated with improved survival.

【 授权许可】

CC BY   
© The Author(s). 2016