Herlyn-werner-wunderlich syndrome: MRI findings, radiological guide (two cases and literature review), and differential diagnosis

BMC Medical Imaging

Case Report

Claudia L Piccolo¹  Rosario F Grasso¹  Ilaria Sansoni¹  Roberto L Cazzato¹  Valerio Di Paola¹  Riccardo Del Vescovo¹  Sofia Battisti¹  Bruno Beomonte Zobel¹ 

[1] Department of Radiology, Campus Bio-Medico Univeristy of Rome, Italy;

关键词: Endometriosis;    Methaemoglobin;    Vaginal Septum;    Magnetic Resonance Image Exam;    Rudimentary Horn;   

DOI  :  10.1186/1471-2342-12-4

 received in 2011-04-09, accepted in 2012-03-09,  发布年份 2012

来源: Springer

【 摘 要 】

BackgroundHerlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract involving Müllerian ducts and Wolffian structures, and it is characterized by the triad of didelphys uterus, obstructed hemivagina and ipsilateral renal agenesis. It generally occurs at puberty and exhibits non-specific and variable symptoms with acute or pelvic pain shortly following menarche, causing a delay in the diagnosis. Moreover, the diagnosis is complicated by the infrequency of this syndrome, because Müllerian duct anomalies (MDA) are infrequently encountered in a routine clinical setting.Cases presentationtwo cases of HWW syndrome in adolescents and a differential diagnosis for one case of a different MDA, and the impact of magnetic resonance (MR) imaging technology to achieve the correct diagnosis.ConclusionsMR imaging is a very suitable diagnostic tool in order to perform the correct diagnosis of HWW syndrome.

【 授权许可】

CC BY   
© Del Vescovo et al; licensee BioMed Central Ltd. 2012