Cor triatriatum and lipomatous hypertrophy of the interatrial septum in the elderly: a case report

Cardiovascular Ultrasound

Case Report

Giuseppe Mercuro¹  Pier Paolo Bassareo¹  Roberto Tumbarello² 

[1] Department of Cardiovascular and Neurological Sciences, University of Cagliari, Cagliari, Italy;Division of Paediatric Cardiology, G. Brotzu Hospital, Cagliari, Italy;

关键词: Pulmonary Vein;    Left Atrium;    Atrial Septum;    Interatrial Septum;    Transoesophageal Echocardiography;   

DOI  :  10.1186/1476-7120-8-4

 received in 2010-02-03, accepted in 2010-03-09,  发布年份 2010

来源: Springer

【 摘 要 】

Cor triatriatum is a rare congenital heart defect characterized by the presence of a fibromuscular membrane dividing the left atrium into two distinct chambers. Lipomatous hypertrophy of the atrial septum is an infrequently observed benign abnormality caused by large fatty tissue deposits in the interatrial septum. An increased incidence of atrial arrhythmias is described in both pathologies, while a significant obstruction of blood flow mimicking mitral stenosis is typically manifested in cor triatriatum. We report the case of a 75-year-old woman with a previously undescribed association of the above stated abnormalities detected by both transthoracic and transeosophageal echocardiography. Diagnosis was confirmed by means of computed tomography. The singular physiologic and anatomic factors underlying survival until such a late age are described. The diagnostic, therapeutic and surgical management is discussed and a short review of the literature performed.

【 授权许可】

CC BY   
© Bassareo et al; licensee BioMed Central Ltd. 2010