Anaesthetic considerations of adults with Morquio's syndrome - a case report

BMC Anesthesiology

Case Report

Maria B Donnelly¹  Anne Marie McLaughlin¹  Kieran Foley¹  Muhammad Farooq¹ 

[1] Department of Anaesthesia and Critical Care, Adelaide and Meath National Children Hospital Dublin, Dublin, Ireland;

关键词: Atracurium;    Obstructive Sleep Apnoea;    Mucopolysaccharide;    Odontoid Process;    Atlantoaxial Instability;   

DOI  :  10.1186/1471-2253-10-2

 received in 2009-05-01, accepted in 2010-02-26,  发布年份 2010

来源: Springer

【 摘 要 】

BackgroundThe anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx.Case presentationHerein we describe the anaesthetic considerations and management of a 26 year old adult with Morquio syndrome, who presented for an elective hip replacement.ConclusionThis report details an awake fiberoptic intubation in an adult with Morquio syndrome. We recommend that this approach be considered in patients with Morquio syndrome undergoing general anaesthesia.

【 授权许可】

CC BY   
© McLaughlin et al; licensee BioMed Central Ltd. 2010