CD34 + tumours of the orbit including solitary fibrous tumours: a six-case series

BMC Ophthalmology

Case Report

Suk-Woo Yang¹  Ji Sun Paik¹  Gyeong Sin Park²  Su Kyung Jung³ 

[1] Department of Ophthalmology and Visual Science, College of Medicine, Seoul St. Mary’s Hospital, The Catholic University of Korea, 505 Banpo-dong, Seocho-gu, 137–701, Seoul, Korea;Department of Pathology, College of Medicine, Seoul St. Mary’s Hospital, The Catholic University of Korea, Seoul, Korea;Eye clinic, Hospital, National Cancer center, Gyeonggi-do, Korea;

关键词: CD34;    Solitary fibrous tumour;    Fibrous histiocytoma;    Haemangiopericytoma;    Mesenchymal tumour;   

DOI  :  10.1186/s12886-017-0455-x

 received in 2016-11-04, accepted in 2017-04-22,  发布年份 2017

来源: Springer

【 摘 要 】

BackgroundTo report six cases of CD34+ fibroblastic mesenchymal tumours, which are uncommon neoplasms in the orbit.Case presentationSix patients presenting with proptosis and palpable mass who were later diagnosed with fibrous solitary tumours, fibrous histocytoma or haemangiopericytoma in the orbit were included. All patients received radiologic examinations and surgical excision for histopathology and immunohistochemistry examinations. Five patients had no recurrence after a minimum follow-up of 12 months. One patient (case 6) experienced recurrence twice, and had debulking surgeries each time. At present, the patient still has remnant tumour in the orbit, but no growth has been detected during the past two years. The tumour size will be closely monitored.ConclusionsEven though fibroblastic tumours are rarely found in the orbit, they can present as a palpable mass with proptosis. Complete surgical excision is important for long-term prognosis, and immunohistochemical study is helpful for confirming pathologic diagnosis.

【 授权许可】

CC BY   
© The Author(s). 2017