Intravascular leiomyomatosis with cardiac extension, a case report

Journal of Cardiothoracic Surgery

Case Report

Vladimir Ullauri Solórzano¹  Gerardo Dávalos Dávalos²  Santiago Endara Aguirre²  Gabriel A. Molina³  Sofía Zárate León⁴  Fernando Terán Camacho⁵  Ligia Redrobán Armendáriz⁶  Juan Garcés Garcés⁷ 

[1] Cardiology Service, Internal Medicine Department, Hospital Metropolitano, Quito, Ecuador;Cardiothoracic Surgery, Surgery Department, Hospital Metropolitano, Quito, Ecuador;General Surgery, Surgery Department, Hospital Metropolitano & USFQ, Quito, Ecuador;General Surgery, Surgery Department, Hospital Metropolitano, Quito, Ecuador;Oncological Surgery, Surgery Department, Hospital Metropolitano, Quito, Ecuador;Pathology Service, Internal Medicine Department, Hospital Metropolitano, Quito, Ecuador;Radiology Service, Internal Medicine Department, Hospital Metropolitano, Quito, Ecuador;

关键词: Intravascular leiomyomatosis (IVL);    Heart Tumor;    Vascular growth;   

DOI  :  10.1186/s13019-023-02344-9

 received in 2022-11-25, accepted in 2023-08-07,  发布年份 2023

来源: Springer

【 摘 要 】

BackgroundIntravascular leiomyomatosis (IVL) is a histologically benign smooth muscle tumor arising from the uterus that can spread through the pelvic veins and, on rare occasions, extend as far as the heart via the inferior vena cava. Despite its benign characteristics, it can behave like a malignant tumor leading to significant morbidity and even mortality if left untreated.Case presentationThe patient is a 42-year-old woman with a past medical history of uterine leiomyomas. She presented with heavy bleeding and frequent spotting; therefore, she went to her gynecologist. After further evaluation, a mass within the uterus that expanded into the pelvic veins, inferior vena cava, and right atrium was discovered. After the complete removal of the mass, the patient underwent full recovery. IVL with cardiac extension was the final diagnosis.ConclusionAlthough IVL is rare, it must be considered in women who underwent previous hysterectomies or myomectomies and present with symptoms of right heart failure. The ideal therapy will need the aid of a multidisciplinary team and will depend on the patient’s symptoms, previous operative history, the tumor’s extension, and resectability.

【 授权许可】

CC BY   
© BioMed Central Ltd., part of Springer Nature 2023

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