Case report and review of the literature: rare fetus-in-fetu presenting as oropharyngeal epignathus

Frontiers in Surgery

Surgery

Georg Henze¹  Michael Reinehr²  Dominic Good³  Claudine Gysin³  Hergen Friedrich³  Daniel Runggaldier⁴ 

[1] Department of Anesthesia, University Children’s Hospital, Zürich, Switzerland;Department, of Otorhinolaryngology, Head & Neck Surgery, University Hospital Zürich, University of Zurich, Zürich, Switzerland;Institute for Pathology and Molecular Pathology, University Hospital Zurich, Zurich, Switzerland;Division of Pediatric Otolaryngology, University Children's Hospital, Zurich, Switzerland;Division of Pediatric Otolaryngology, University Children's Hospital, Zurich, Switzerland;Department, of Otorhinolaryngology, Head & Neck Surgery, University Hospital Zürich, University of Zurich, Zürich, Switzerland;

关键词: heteropagus;    asymmetric twin;    fetus in fetu (FIF);    neonate airway;    epignathus;   

DOI  :  10.3389/fsurg.2023.1122327

 received in 2022-12-12, accepted in 2023-04-12,  发布年份 2023

来源: Frontiers

【 摘 要 】

An epignathus is caused by a continuous spectrum of masses of the oral cavity or oropharynx ranging in its entity from mature teratoma to the exceedingly rare fetus-in-fetu. Due to its location, regardless of the entity, the occurrence of an epignathus is frequently associated with life threatening airway obstruction. Here we demonstrate a case of a fetus-in-fetu presenting as an epignatus. We describe its successful management and review the available literature. Early diagnosis and knowledge of the preoperative workup are essential to enable a multidisciplinary management. Once the airway is secured, surgical excision is the treatment of choice often resulting in a good clinical outcome and prognosis.

【 授权许可】

Unknown   
© 2023 Runggaldier, Reinehr, Friedrich, Henze, and Gysin.