Pneumatosis cystoides intestinalis in dermatomyositis: a case series report and literature review

Frontiers in Immunology

Immunology

Shuo Chen¹  Ling Zhang²  Jianwen Liu³  Xin Lu⁴  Shanshan Li⁴ 

[1] Department of Gastroenterology, China-Japan Friendship Hospital, Beijing, China;Department of Radiology, China-Japan Friendship Hospital, Beijing, China;Department of Rheumatology and Immunology, Fujian Provincial Hospital, Shengli Clinical Medical College of Fujian Medical University, Fuzhou, China;Department of Rheumatology, Key Laboratory of Myositis, China-Japan Friendship Hospital, Beijing, China;

关键词: pneumatosis cystoides intestinalis;    dermatomyositis;    asymptomatic;    pathological mechanism;    prognosis;   

DOI  :  10.3389/fimmu.2023.1194721

 received in 2023-03-27, accepted in 2023-05-09,  发布年份 2023

来源: Frontiers

【 摘 要 】

Pneumatosis cystoides intestinalis (PCI) in adult dermatomyositis (DM) is rarely described. This report aimed to describe the clinical features and prognosis of PCI in six adult patients with DM (four with anti-MDA5 antibodies, one with anti-SAE antibodies, and one with anti-TIF-1γ antibodies). Except for one patient with transient abdominal pain, the remaining five patients were asymptomatic. PCI occurred in the ascending colon in all patients, of whom five had free gas in the abdominal cavity. No patients received excessive treatment, and PCI disappeared in four patients during the follow-up. Additionally, we reviewed previous studies on this complication.

【 授权许可】

Unknown   
Copyright © 2023 Liu, Zhang, Chen, Lu and Li