Temporal bone manifestation of primary extranodal Rosai–Dorfman disease: a case report

Journal of Medical Case Reports

Case Report

M. Hyrcza¹  J. Chau²  F. Ramazani²  E. Koonar² 

[1] Department of Pathology and Laboratory Medicine, Arnie Charbonneau Cancer Institute, University of Calgary, Calgary, Canada;Division of Otolaryngology-Head and Neck Surgery, Department of Surgery, Cumming School of Medicine, University of Calgary, Calgary, Canada;

关键词: Temporal bone;    Rosai–Dorfman disease;    Histiocytosis;    Case report;   

DOI  :  10.1186/s13256-023-03790-8

 received in 2022-10-30, accepted in 2023-01-24,  发布年份 2023

来源: Springer

【 摘 要 】

BackgroundRosai–Dorfman disease is a rare benign histiocytic disorder characterized in most cases by painless cervical adenopathy. Less than 10% of extranodal cases involve bony lesions. Primary bone Rosai–Dorfman disease in the absence of nodal disease is extremely rare.Case presentationA 48 year-old Caucasian male presented with progressive right-sided otalgia, tinnitus, vertigo, and hearing loss. A right temporal bone lytic lesion was detected on diagnostic imaging. Resection of the lesion and histopathological examination revealed Rosai–Dorfman disease.ConclusionsRosai–Dorfman disease primary bone lesions are an atypical presentation of a rare disease. This is the second reported case of Rosai–Dorfman disease arising within the temporal bone. This case study reveals that Rosai–Dorfman disease should be considered for patients presenting with inflammatory/lytic lesions of the temporal bone, in cases where infection and malignancy have been excluded.

【 授权许可】

CC BY   
© Crown 2023

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