Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report

BMC Ophthalmology

Case Report

Zhiqiao Liang¹  Huijuan Wu¹  Kangyi Yang¹  Kun Lv¹  Yao Ma¹  Xuanzhu Chen¹ 

[1] Department of Ophthalmology, Peking University People’s Hospital, Beijing, China;Eye Diseases and Optometry Institute, Beijing Key Laboratory of Diagnosis and Therapy of Retinal and Choroid Diseases, College of Optometry, Peking University Health Science Center, Beijing, China;

关键词: Pigmented paravenous retinochoroidal atrophy;    Acute angle-closure glaucoma;    Unilateral;   

DOI  :  10.1186/s12886-023-02922-4

 received in 2022-12-21, accepted in 2023-04-14,  发布年份 2023

来源: Springer

【 摘 要 】

BackgroundPigmented paravenous retinochoroidal atrophy (PPRCA) is an uncommon fundus disease characterized by perivenous aggregations of pigment clumps and retinochoroidal atrophy distributed along the retinal veins. We report a Chinese female case of unilateral PPRCA with acute angle-closure glaucoma (AACG).Case presentationA 50-year-old Chinese female presented with vision loss and elevated intraocular pressure (IOP) in the right eye and then underwent trabeculectomy. She referred to our clinic for further evaluation and treatment. The funduscopic examination revealed grayish retinochoroidal atrophy and osteocyte-like pigment clumping lesions along the retinal veins and peripapillary preretinal hemorrhage in the right eye. The patient also presented with AACG in the same eye on the basis of past medical history of acute attack, shallow anterior chamber depth (ACD), narrow angle showed by ultrasound biomicroscopy (UBM) and glaucomatous neuropathy identified by optical coherence tomography (OCT). Other examinations like fluorescein fundus angiography (FFA), electroretinogram (ERG) and electrooculography (EOG) all confirmed the aforementioned diagnose.ConclusionPPRCA is a rare disease, uncommon in females and symmetrical in both eyes. We present a rare case of unilateral PPRCA accompanied with AACG.

【 授权许可】

CC BY   
© The Author(s) 2023

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