Cervical Primitive Neuroectodermal Tumor in an Adult: Case Report and Literature Review

Brazilian Neurosurgery

article

Guilherme dos Santos de Alencar¹  Maria Eduarda Turczyn De Lucca²  Felipe Antonio Torres Mazzo³  Milena Massumi Konozoe⁴  Eduardo Talib Bacchi Jaouhari⁵  Rodrigo Leite de Morais⁵  Carlos Eliseu Barcelos⁵  Rosângela Stadnick Lauth de Almeida Torres⁶ 

[1] Department of Neurosurgery, Curso de Medicina, Universidade Federal do Paraná;Universidade Positivo;Medicine Program, Pontifícia Universidade Católica do Paraná;Department of Pathology, Hospital Erasto Gaertner;Department of Neurosurgery, Hospital Erasto Gaertner;Department of Pharmaceutical Sciences, Faculdade de Farmácia, Universidade Positivo

关键词: primitive neuroectodermal tumors;    adult;    medulloblastoma;   

DOI  :  10.1055/s-0042-1742709

学科分类：社会科学、人文和艺术（综合）

来源: Thieme

【 摘 要 】

Introduction Primitive neuroectodermal tumors are rare neoplasms of the central nervous system that occur in children, with few reports in adults. These tumors are found most often in the cerebral hemispheres, with spinal cord disorders being rare.Case Report A 71-year-old man with motor and sensory deficits in the upper limbs, cervical pain, and urinary incontinence presented to the Neurosurgery Service. The physical examination revealed grade-III motor strength on the right side, grade IV- on the left upper limb, and grade IV+ on the left lower limb. A magnetic resonance imaging scan showed an expansive intramedullary lesion with a C3-C4 epicenter. Spinal decompression, lesional biopsy, and adjuvant radiotherapy were performed. The anatomopathological report showed a primitive neuroectodermal tumor. After a new treatment with adjuvant radiotherapy (20 × 1.8 Gy in the skull and neuroaxis and 5 × 1.8 Gy in tumor boost), the patient progressed without recurrence.Conclusion Since the characteristics of the tumor are similar to those of medulloblastoma, it is necessary to expand the studies on these lesions, to better understand their pathophysiology and list better diagnostic and therapeutic methods, in addition to those already available.

【 授权许可】

CC BY|CC BY-NC-ND