Retrograde Type A Aortic Dissection 48 Hours after TEVAR in a Patient with a Delayed Diagnosis of Vascular Ehlers-Danlos Syndrome

AORTA

article

Ian Diebels¹  Jeroen M.H. Hendriks¹  Joke Durnez¹  Bernard P. Paelinck²  Haroun El Addouli²  Steven Laga²  Bart L. Loeys² 

[1] Department of Thoracic and Vascular Surgery, Antwerp University Hospital;European Reference Network Qualified Aorta Clinic of the Antwerp University Hospital, Antwerp University Hospital;Department of Cardiology, Antwerp University Hospital;Department of Radiology, Antwerp University Hospital;Department of Cardiac Surgery, Antwerp University Hospital;Department of Genetic Medicine, Antwerp University Hospital

关键词: acute aortic syndrome;    aortic dissection;    thoracic endovascular aortic repair;    vascular Ehlers-Danlos syndrome;    connective tissue disorder;   

DOI  :  10.1055/s-0042-1749171

来源: Thieme

【 摘 要 】

We report a case of a fatal retrograde Type A aortic dissection following thoracic endovascular aortic repair (TEVAR). The patient was diagnosed with vascular Ehlers-Danlos syndrome (vEDS) only postoperatively, which is a relative contraindication for TEVAR. The patient had no major or minor criteria for vEDS. This case report emphasizes pitfalls of TEVAR in patients with a connective tissue disorder.

【 授权许可】

Unknown