期刊论文详细信息
AORTA | |
Retrograde Type A Aortic Dissection 48 Hours after TEVAR in a Patient with a Delayed Diagnosis of Vascular Ehlers-Danlos Syndrome | |
article | |
Ian Diebels1  Jeroen M.H. Hendriks1  Joke Durnez1  Bernard P. Paelinck2  Haroun El Addouli2  Steven Laga2  Bart L. Loeys2  | |
[1] Department of Thoracic and Vascular Surgery, Antwerp University Hospital;European Reference Network Qualified Aorta Clinic of the Antwerp University Hospital, Antwerp University Hospital;Department of Cardiology, Antwerp University Hospital;Department of Radiology, Antwerp University Hospital;Department of Cardiac Surgery, Antwerp University Hospital;Department of Genetic Medicine, Antwerp University Hospital | |
关键词: acute aortic syndrome; aortic dissection; thoracic endovascular aortic repair; vascular Ehlers-Danlos syndrome; connective tissue disorder; | |
DOI : 10.1055/s-0042-1749171 | |
来源: Thieme | |
【 摘 要 】
We report a case of a fatal retrograde Type A aortic dissection following thoracic endovascular aortic repair (TEVAR). The patient was diagnosed with vascular Ehlers-Danlos syndrome (vEDS) only postoperatively, which is a relative contraindication for TEVAR. The patient had no major or minor criteria for vEDS. This case report emphasizes pitfalls of TEVAR in patients with a connective tissue disorder.
【 授权许可】
Unknown
【 预 览 】
Files | Size | Format | View |
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RO202307130003519ZK.pdf | 1009KB | download |