Cardiac MR imaging reveals L-type transposition of the great vessels and failing right heart

Radiology Case Reports

article

Lindsay Everett¹  Ishan Parikh¹  Pritee Taxak¹  Brittany Albers¹  Jonathan Joshi¹ 

[1]School of Medicine, University of Louisville

关键词: Cardiac MRI;    Transposition;    Congenital Heart Defect;    Heart Failure;   

DOI  :  10.1016/j.radcr.2022.07.094

学科分类：生物化学工程

来源: University of Washington * Department of Radiology

【 摘 要 】

L-type transposition of the great vessels is a rare congenital heart disease in which both the great arteries and the ventricular chambers are reversed. Because this condition preserves a physiologic circulatory pathway, it can be challenging to diagnose in infants with no concurrent cardiac abnormalities. Early detection is essential, however, because these patients will eventually experience severe complications, as the structural right ventricle is unable to function long-term in the systemic position. We report a rare case of L-type transposition of the great vessels in a 32-year-old male who presented in adulthood with tachycardia and palpitations . The initial echocardiogram was inconclusive. Further imaging (cardiac MRI & transesophageal echocardiogram) revealed the inverted anatomy due to the presence of key morphological features, such as the malposed great vessels along with the moderator band and prominent trabeculae within the right ventricle, which was functioning systemically.

【 授权许可】

CC BY|CC BY-NC-ND