Neuro-Behcet's syndrome: Case report and literature review

Radiology Case Reports

article

Brian Peine¹  Christian Figueroa¹  Natasha Robinette¹ 

[1] Central Michigan University College of Medicine, 1280 East Campus Dr

关键词: Neuro-Behcet disease;    Behcet syndrome;    Pons;    Ventral medulla;    Hyperintense punctate foci;    MRI;   

DOI  :  10.1016/j.radcr.2022.05.070

学科分类：生物化学工程

来源: University of Washington * Department of Radiology

【 摘 要 】

Behcet's disease (BD) is a multisystem, autoimmune vasculitis disorder affecting small, medium, and large blood vessels, with poorly understood pathogenesis. It commonly presents with recurrent aphthous ulcers , genital ulcers , skin lesions, and bilateral uveitis . Neurological symptoms are present in less than 10% of cases and develop, on average, 5-6 years after the first non-neurological symptoms. This presentation, known as Neuro-Behcet's disease (NBD), is associated with a worse prognosis of BD. Treatment for NBD is dependent on the severity of symptoms and the presence of other systemic manifestations but often initially involves glucocorticoids and a disease-modifying agent. This case report presents a 44-year-old female patient, previously diagnosed with BD, who presented with neurological symptoms and MRI findings consistent with NBD.

【 授权许可】

CC BY|CC BY-NC-ND