Pseudoxanthoma Elasticum and Light-Chain Amyloidosis

European Journal of Inflammation

Letter to the Editor

C. Abruzzese¹  G. Cortesi¹  M. Carlesimo¹  E. Mari²  G. La Verde³  A. Moscetti³  M. Lombardi⁴  A.M. Ciccone⁵  C. Poggi⁵ 

[1] NESMOS, U.O.C. Dermatology, Sant'Andrea Hospital University of Rome “Sapienza”, Faculty of Medicine and Psychology, Rome, Italy;U.O.C. Clinica Dermatologica Dipartimento di Medicina Interna e Specialita Mediche University of Rome “Sapienza”, Rome, Italy;U.O.C. Ematology Sant Andrea Hospital University of Rome “Sapienza”, Faculty of Medicine and Psycology, Rome, Italy;U.O.C. Histopathology, Sant Andrea Hospital University of Rome “Sapienza”, Faculty of Medicine and Psychology, Rome, Italy;U.O.C. Thorax Surgery, Sant'Andrea Hospital University of Rome “Sapienza”, Faculty of Medicine and Psychology, Rome, Italy;

关键词: pseudoxanthoma elasticum;    light-chain amyloidosis;    elastic fibers;    monoclonal gammopathy;   

DOI  :  10.1177/1721727X1201000329

 received in 2012-04-13, accepted in 2012-09-21,  发布年份 2012

来源: Sage Journals

【 摘 要 】

Pseudoxanthoma elasticum is a heritable disorder of connective tissue characterized by cutaneous, vascular and ocular changes that result from the accumulation of fragmented elastic fibres. Even though the etiopathogenesis is not still completely understood, in recent years in literature some Authors have considered pseudoxanthoma elasticum as a metabolic disorder. We present the case of a 45-year-old man affected by pseudoxanthoma elasticum and light-chain amyloidosis and we discuss the possible reasons that led to this association.

【 授权许可】

Unknown   
© 2012 SAGE Publications