Idiopathic Pulmonary Fibrosis: Diagnosis and Clinical Manifestations

Clinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine

Review

Yutaro Nakamura¹  Takafumi Suda¹ 

[1]Department of Internal Medicine, Hamamatsu University School of Medicine, Hamamatsu, Shizuoka, Japan.

关键词: idiopathic pulmonary fibrosis;    signs;    symptoms;    clinical course;    prognosis;    clinical presentation;   

DOI  :  10.4137/CCRPM.S39897

 received in 2016-04-11, accepted in 2016-07-05,  发布年份 2015

来源: Sage Journals

【 摘 要 】

Idiopathic pulmonary fibrosis (IPF) is a parenchymal lung disease characterized by progressive interstitial fibrosis. The clinical course of IPF can be unpredictable and may be punctuated by acute exacerbations. Although much progress is being made in unraveling the mechanisms underlying IPF, effective therapy for improving survival remains elusive. Longitudinal disease profiling, especially in terms of clinical manifestations in a large cohort of patients, should lead to proper management of the patients and development of new treatments for IPF. Appropriate multidisciplinary assessment in ongoing registries is required to achieve this. This review summarizes the current status of the diagnosis and clinical manifestations of IPF.

【 授权许可】

CC BY-NC   
© 2015 SAGE Publications.

【 图 表 】

Graph 3.

Figure 1.