A Rare Case of Double-Chambered Right Ventricle Associated with Ventricular Septal Defect and congenital Absence of the Pulmonary Valve

Clinical Medicine Insights: Circulatory, Respiratory and Pulmonary Medicine

Short Report

Wissam Hoyek¹  Georges Khoueiry¹  Nidal Abi Rafeh¹  Tariq Bhat¹  Mustafain Meghani²  Mohmad Tantray²  Mokhtar Abdallah² 

[1] Department of Cardiology, Staten Island University Hospital, Staten Island, NY.;Department of Medicine, Staten Island University Hospital, Staten Island, NY.;

关键词: cardiology;    magnetic resonance imaging;    echocardiography;    doubled-chambered right ventricle;    ventricular septal defect;   

DOI  :  10.4137/CCRPM.S11174

来源: Sage Journals

【 摘 要 】

Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve, a rare form of congenital infundibular pulmonary stenosis. In addition to ventricular septal defect, our patient had congenital absence of the pulmonary valve, which is very unusual and has never been reported to our knowledge.

【 授权许可】

CC BY-NC   
© 2014 SAGE Publications.