Malignant and Metastatic Pheochromocytoma: Case Report and Review of the Literature

Urology Case Reports

关键词: Pheochromocytoma;    Neuroendocrine;    Adrenal;    Renal;   

DOI  :  10.1016/j.eucr.2014.05.001

来源: DOAJ

【 摘 要 】

Pheochromocytomas are rare neuroendocrine tumors. Although predominantly occurring in the adrenal glands, these tumors can present anywhere along the sympathetic chain. Indeed, classical teaching states that 10% of pheochromocytomas are extra-adrenal and 10% are malignant. We report a case of a 61-year-old female who underwent presumptive cytoreductive nephrectomy and adrenalectomy for renal carcinoma but was instead found to have malignant pheochromocytoma. Proper identification, surgical extirpation, and follow-up are imperative for treatment. We review the classic and current literature regarding management of this uncommon tumor.

【 授权许可】

Unknown