Kazabach–Merritt syndrome without skin manifestations in an infant

Rossijskij Vestnik Perinatologii i Pediatrii

L. V. Bregel¹  N. Yu. Rudenko¹  A. E. Matyunova²  A. O. Barakin²  O. S. Efremova²  T. S. Korinets³ 

[1] Regional Children’s Hospital;Irkutsk State Medical Academy of Continuous Professional Education branch of Russian Medical Academy of ContinuousProfessional Education;Regional Children’s Hospital;

关键词: infants;    kazabach–merritt syndrome;    vascular tumor;    hemopericardium;    thrombocytopenia;   

DOI  :  10.21508/1027-4065-2022-67-1-120-124

来源: DOAJ

【 摘 要 】

The authors observed Kazabach–Merritt syndrome in an infant with an intrathoracic localization of the tumor without vascular manifestations on the skin. The disease was detected by signs of hemopericardium during screening echocardiography in combination with thrombocytopenia and relapses of intrathoracic bleeding. The diagnosis was confirmed by MSCT and biopsy data. Treatment with beta-blockers and chemotherapy resulted in tumor reduction and the disappearance of clinical symptoms.

【 授权许可】

Unknown