Rare case of recurrent Kikuchi-Fujimoto disease

Journal of Medical and Scientific Research

Prathibha¹  Satish Rao²  Suvarna Shilpa³  Sarath Chandra Mouli⁴ 

[1] B;I;S;Veeravalli;

关键词: Kikuchi-Fujimoto disease;    histiocytic necrotizing lymphadenitis;    plasmacytoid dendritic cells;    hydroxychloroquine;   

DOI  :  10.17727/JMSR.2017/5-25

来源: DOAJ

【 摘 要 】

Kikuchi-Fujimoto disease (KFD), or histiocytic necrotizing lymphadenitis, is a rare benign, self-limiting cervical lymphadenitis of unknown etiology. It closely mimics infective and immunological disorders. Here a rare case of recurrent KFD in a 13-year-old girl is presented. This girl presented with low grade fever at night times with sweating of 20 days duration and with painful right cervical lymphadenopathy. She had a bad history of recurrent episodes of lymphadenopathy seven years ago again after two years ago she was treated with empirical ATT. Her routine blood and urine tests were normal. Tests for infection and autoimmunity were negative. Histopathological examination is suggestive of Kikuchi lymphadenitis. Thus, she was diagnosed as a case of recurrent Kikuchi and was treated with oral steroids and hydroxychloroquine (HCQ). To the best of our knowledge, this is the first case of recurrent Kikuchi observed in an Indian patient and treated with Hydroxychloroquine and low dose steroids.

【 授权许可】

Unknown